Arrhythmogenic right ventricular cardiomyopathy: A case report and review of literature

Shabarinath S, Dayasagar Rao V

Pdf Page Numbers :- 65-71

  ¹Department of Cardiology, Krishna Institute of Medical Sciences, Minister Road, Secunderabad-500003, Telangana, India

Received 23 January 2015; Revised 15 March 2016; Accepted 22 March 2016; Published 30 March 2016

Citation:Shabarinath S, Dayasagarao V. Arrhythmogenic right ventricular cardiomyopathy: A case report and review of literature. J Med Sci Res. 2016; 4(2):65-71.DOI: http://dx.doi.org/10.17727/JMSR.2016/4-016

Copyright: © 2016 Shabarinath S, et al. Published by KIMS Foundation and Research Centre. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution and reproduction in any medium, provided the original author and source are credited.

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Abstract

  Abstract

Arrhythmogenicright ventricular cardiomyopathy (also called arrhythmogenic RV dysplasia [ARVD]) is a heterogeneous inherited disease that results in fibrofatty infiltration of the right ventriclepredominant, although the disease can also affect the left ventricle (typically the posterior portion). It is a rare and life threatening cause of sudden cardiac death. ECG often carries the first clue to its diagnosis and a high degree of suspicion needs to be maintained to identify this condition in young patients presenting with syncope. We are presenting one such case of an young male who presented with syncope and one episode of documented VT who on evaluation turned out to be a case of ARVD.

Keywords: ARVD/ARVC;ventricular arrhythmias;sudden death;cardiac MRI; ICD